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KMID : 1035220180100020041
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Korean Journal of Neuromuscular Disorders
2018 Volume.10 No. 2 p.41 ~ p.44
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Lewis-Sumner Syndrome; Extensive Cranial and Cervical Root Involvement on MR Imaging
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Kim Sun-Young
Shin Ha-Young
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Abstract
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A 33-year-old woman, previously diagnosed with multifocal acquired demyelinating sensory and motor neuropathy, or Lewis-Sumner syndrome (LSS), presented with diffuse multifocal nerve root swelling at cervical 3th to 7th resembling with neurofibroma. Upon nerve conduction investigations, multifocal conduction block in the upper limb were discovered. In addition, a right mandibular branch of trigeminal nerve hypertrophy resembling schwannoma was found Treatment with intravenous immunoglobulin and steroid improved her symptoms. The observed hypertrophy in the right mandibular branch of the trigeminal nerve was correlated with her symptoms. This study presents a case of LSS mimicking neurofibroma with coexisting cranial and peripheral nerve involvement, emphasizing the usefulness of the magnetic resonance imaging.
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KEYWORD
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Polyradiculoneuropathy, chronic inflammatory demyelinating, Neurofibroma
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